Maroteaux-Lamy syndrome

[măr′ə-tōlä-mē, mä-rô-]

n.

An inherited defect in mucopolysaccharide metabolism characterized by excretion of dermatan sulfate in the urine, retarded growth, lumbar kyphosis, sternal protrusion, knock-knee, and usually enlargement of the liver and spleen.type VI mucopolysaccharidosis

The American Heritage® Stedman's Medical Dictionary Copyright © 2002, 2001, 1995 by Houghton Mifflin Company. Published by Houghton Mifflin Company.