Wolman's disease

[ wôlmənz ]


An inherited disorder of lipid metabolism caused by a deficiency of lysosomal acid lipase and resulting in the widespread accumulation of cholesterol esters and triglycerides in the internal organs.

The American Heritage® Stedman's Medical Dictionary Copyright © 2002, 2001, 1995 by Houghton Mifflin Company. Published by Houghton Mifflin Company.